Renal Rhabdomyosarcoma, Pleomorhic Variant in a 61-year old Male

Renal Rhabdomyosarcoma, Pleomorhic Variant in a 61-year old Male
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Title:Renal Rhabdomyosarcoma, Pleomorhic Variant in a 61-year old Male
Author/Abstract:

Sandino Lorenzo Cu, MD; Enrique Ian S. Lorenzo, MD, FPUA and Edgardo L. Reyes, MD, FPUA
Department of Urology, Jose R. Reyes Memorial Medical Center

Renal rhabdhomyosarcoma is a rare subtype of renal sarcoma in adults that arise from skeletal muscle
progenitor cells. Primary rhabdomyosarcomas are usually seen in the pediatric population and
extremely rare in adults. This is a case of 61 year old, male who presented with a 3 week history of a
palpable left upper quadrant mass accompanied by early satiety, anorexia, weight loss and dysuria.
Ultrasound of whole abdomen revealed a hydronephrotic left kidney with no noted lithiasis and
unremarkable right kidney. CT scan of the abdomen was chronic cystic pyelonephritis vs renal
neoplasm, left paraaortic or perirenal lymphadenopathy suggestive of regional node metastasis. The
case was diagnosed as Left Renal New Growth with consideration of Renal Cell Carcinoma
(T2bN1M0). Hence the patient underwent cytoreductive nephrectomy. The histopathologic report
revealed pleomorphic rhabdomyosarcoma. Literature review of renal rhabdomyosarcoma regarding
symptomatology, diagnostic modality, treatment standard, adjuvant therapy and prognosis was done.

Key words: Rhabdomyosarcoma, pleomorphic, renal sarcoma, embryonal rhabdomyosarcoma

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