A 32-year old Female Diagnosed with Primary Adrenal Hemangiopericytoma

A 32-year old Female Diagnosed with Primary Adrenal Hemangiopericytoma
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Title:A 32-year old Female Diagnosed with Primary Adrenal Hemangiopericytoma
Author/Abstract:

Luis Antonio R. Balajadia, MD and Michael Jonathan S. Latayan, MD, FPUA
Department of Urology, Southern Philippines Medical Center, Davao City

Hemangiopericytomas are rare tumors originating from pericytes in the wall of capillaries. It is a type
of soft tissue sarcoma which commonly involves the lower extremities, pelvic retroperitoneum, and
head & neck. A 32-year old female presented with a 5 year history of slowly-growing right flank
mass. Physical examination findings showed a bulging right flank mass extending anteriorly,
approximately 15cm x 15cm, firm, movable, nontender mass on bimanual examination. CT-scan
with IV contrast revealed a large suprarenal mass, right. She underwent adrenalectomy with en-bloc
nephrectomy, right with uneventful post-operative course. Histopathology of the specimen was read
as hemangiopericytoma. Further testing by Fluorescence In-Situ Hybridization confirmed the
diagnosis. Metastatic work-up was negative. Hence, this is the first reported case of primary adrenal
hemangiopericytoma. Surgical removal is the mainstay of treatment of hemangiopericytomas.
Radiotherapy and chemotherapy have no role in the management of the disease.

Key words: hemangiopericytoma, adrenal tumor, urologic malignancy, pericytes

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