Rhabdoid Tumor in a Nine-Year Old Boy: A Rare Tumor of the Urinary Bladder

Rhabdoid Tumor in a Nine-Year Old Boy: A Rare Tumor of the Urinary Bladder
PropertyValue
Title:Rhabdoid Tumor in a Nine-Year Old Boy: A Rare Tumor of the Urinary Bladder
Author/Abstract:
Roderick P. Arcinas, MD and David T. Bolong, MD, FPUA
Section of Urology, Department of Surgery, University of Santo Tomas Hospital

A 9 year old boy presented with painless gross hematuria 1 month prior to admission. Ultrasound and CT scan of the whole abdomen with contrast showed a 2.6cm x 2.0cm papillary mass on the right posterolateral wall. Initial transurethral biopsy result showed negative for malignancy, fibrovascular tissue with mild chronic and acute inflammation. On repeat cystoscopy, a 4cm x 4cm pedunculated, lobulated mass was located posterolateral encroaching on the right ureteral orifice. Subsequently, a partial cystectomy with distal ureterectomy, right; right-to-left transureteroureterostomy with DJ stent insertion were done. Microscopic and immunostaining results support a diagnosis of rhabdoid tumor. Adjuvant chemotherapy and immunotherapy was given. On followup, there was no evidence of recurrence.

This case emphasizes the need to follow aggressively children with gross hematuria. Biopsy
should include deep biopsies as rhabdoid tumors are infiltrating tumors. Coordination with the
pathologist is of extreme importance since special stainings are needed for confirmation.

Key words: rhabdoid tumor, urinary bladder, treatment, immunohistochemical staining

Phil J Urol 2012; 22(1): 27-32
Filesize: 2.35 MB
Filetype:pdf (Mime Type: application/pdf)